A fibroma arising in the right ventricle outflow tract of a 14 month-old infant was successfully removed. The patient was first seen because of shortness of breath and tachycardia. Pertinent clinical and laboratory findings included a grade Ⅱ/Ⅵ
systolic murmur, blood pressure of 120/60mmHg, slight cardiomegaly on chest X-ray, a mass obstruction the outflow tract of the right ventricle on echocardiography and magnetic resornance imaging.
On october 30, 1992, under cardiopulmonary bypass, a 4cm×3cm×3cm tumor was resected from the right ventricular ourflow tract, together with a portion of the ventrcular wall. Histologically, it was diagnosis as a fibroma. The patient was sent
home
on
the 6th postoperative day following an uneventful recovery form the operation.
Although cardiac fibroma is the second most common cardiac tumor in infancy and childhood, it is usually found in the left ventricle and one arising in the right ventricle is considered rare. Although it is a benign tumor, it could produce a
severe
cardiac dysfuction and even sudden death, depending on its size and location. With the advance in diagnostic techniques and operative management, there is a renewed interest in the early detection and operative removal of these tumors. The case
herein
presented is the first such case successfully managed and reported in the Korean literature.
(Korean J Thorac Cardiovasc Surg 1995;28:491-4)
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